Abstract
This report describes the youngest patient to develop a malignant peripheral nerve sheath tumor arising from a ganglioneuroma (MPNST ex Ganglioneuroma). The patient, a 6-year-old boy, was never irradiated and had no history or stigmata of neurofibromatosis. The report also includes a review of the previously published related cases, and an analysis of the immunohistochemistry and electron microscopy data available to date on the subject.
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de Chadarévian, JP., Pascasio, J., Halligan, G. et al. Malignant Peripheral Nerve Sheath Tumor Arising from an Adrenal Ganglioneuroma in a 6-Year-old Boy. Pediatr. Dev. Pathol. 7, 277–284 (2004). https://doi.org/10.1007/s10024-004-8084-9
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DOI: https://doi.org/10.1007/s10024-004-8084-9