INTRODUCTION
Desmoid tumors are a clinical problem in 12 to 15 percent of patients with familial adenomatous polyposis. There is no predictably effective treatment for intra-abdominal desmoid tumors, which sometimes cause significant complications by their effects on the ureters or bowel. The relative rarity and the clinical heterogeneity of intra-abdominal desmoid tumors make randomized studies difficult to do. In this article a staging system is proposed to make multi-institutional studies easier.
METHODS
Intra-abdominal desmoid tumors can be staged according to their size, clinical presentation and growth pattern.
CONCLUSION
A way of staging intra-abdominal desmoid tumors is proposed to facilitate stratification by disease severity during collaborative studies of various treatments.
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Church, J., Berk, T., Boman, B. et al. Staging Intra-Abdominal Desmoid Tumors in Familial Adenomatous Polyposis: A Search for a Uniform Approach to a Troubling Disease. Dis Colon Rectum 48, 1528–1534 (2005). https://doi.org/10.1007/s10350-005-0018-8
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DOI: https://doi.org/10.1007/s10350-005-0018-8