Summary
An infant girl is described who had cor triatriatum and partial anomalous pulmonary venous connection of the left pulmonary veins to the coronary sinus, the first report of this combination of lesions. The infant also had a Dandy-Walker malformation and multiple facial and intrathoracic hemangiomas. The cardiac diagnosis was made by two-dimensional echocardiography. Cardiac catheterization and angiography confirmed the findings and also demonstrated a persistent left superior vena cava draining to the coronary sinus. The infant underwent successful surgical repair. Partial anomalous pulmonary venous connection and left superior vena cava not infrequently are associated with cor triatriatum. Although two-dimensional echocardiography is sensitive for the detection of cor triatriatum, preoperative cardiac catheterization is necessary to identify unequivocally systemic and pulmonary venous connections.
Article PDF
Similar content being viewed by others
Avoid common mistakes on your manuscript.
References
Arciniegas E, Farooki ZQ, Hakimi M, Perry BL, Green EW (1981) Surgical treatment of cor triatriatum.Ann Thorac Surg 32:571–577
Case Records of the Massachusetts General Hospital (Case 47-1969) (1969)N Engl J Med 281:1178–1187
Freed MD, Rosenthal A, Bernhard WF (1973) Balloon occlusion of a persistent left superior vena cava in the preoperative evaluation of systemic venous return.J Thorac Cardiovasc Surg 65:835–839
Gharagozloo F, Bulkley BH, Hutchins GM (1977) A proposed pathogenesis of cor triatriatum: impingement of the left superior vena cava on the developing left atrium.Am Heart J 94:618–626
Hirsch J, Pierre-Kahn A, Renier D, Sainte-Rose C, Hoppe-Hirsch E (1984) The Dandy-Walker malformation: a review of 40 cases.J Neurosurg 61:515–522
Lee ME, Sade RM (1979) Coronary sinus septal defect: surgical considerations.J Thorac Cardiovasc Surg 78:563–569
Lucas RV Jr (1983) Anomalous venous connections, pulmonary and systemic. In: Adams FH, Emmanouilides GC (eds)Heart disease in infants, children, and adolescents, 3rd edn. Williams and Wilkins, Baltimore, pp 458–490
Niwayama G (1960) Cor triatriatum.Am Heart J 59:291–317
Oglietti J, Cooley DA, Izquierdo JP, Ventemiglia R, Muasher I, Hallman GL, Reul GL Jr (1983) Cor triatriatum: operative results in 25 patients.Ann Thorac Surg 35:415–420
Ostman-Smith I, Silverman NH, Oldershaw P, Lincoln C, Shinebourne EA (1984) Cor triatriatum sinistrum: diagnostic features on cross sectional echocardiography.Br Heart J 51:211–219
Schick EC Jr, Lekakis J, Rothendler JA, Ryan TJ (1985) Persistent left superior vena cava and right superior vena cava drainage into the left atrium without arterial hypoxemia.J Am Coll Cardiol 5:374–378
Schluter M, Langenstein BA, Thier W, Schmiegel W, Krebber H, Kalmar P, Hanrath P (1983) Transesophageal two-dimensional echocardiography in the diagnosis of cor triatriatum in the adult.J Am Coll Cardiol 2:1101–1015
Snellen HA, van Ingen HC, Hoefsmit ECM (1968) Patterns of anomalous pulmonary venous drainage.Circulation 38:45–63
Snider AR, Ports TA, Silverman NH (1979) Venous anomalies of the coronary sinus: detection by M-mode, two-dimensional and contrast echocardiography.Circulation 60:721–727
Thilenius OG, Bharati S, Lev M (1976) Subdivided left atrium: an expanded concept of cor triatriatum sinistrum.Am J Cardiol 37:743–752
Van Praagh R, Corsini I (1969) Cor triatriatum: pathologic anatomy and a consideration of morphogenesis based on 13 postmortem cases and a study of normal development on the pulmonary vein and atrial septum in 83 human embryos.Am Heart J 78:379–405
Wolf WJ (1986) Diagnostic features and pitfalls in the two-dimensional echocardiographic evaluation of a child with cor triatriatum.Pediatr Cardiol 6:211–213
Author information
Authors and Affiliations
Rights and permissions
About this article
Cite this article
Geggel, R.L., Fulton, D.R., Chernoff, H.L. et al. Cor triatriatum associated with partial anomalous pulmonary venous connection to the coronary sinus: Echocardiographic and angiocardiographic features. Pediatr Cardiol 8, 279–283 (1987). https://doi.org/10.1007/BF02427543
Issue Date:
DOI: https://doi.org/10.1007/BF02427543