Abstract
CT findings in pulmonary Gaucher's disease have not been previously reported. Chest radiograph of a patient with pulmonary involvement in type I Gaucher's disease proven by biopsy showed linear and reticulo-nodular opacities. High-resolution CT demonstrated thickening of the interlobular septa and between four and six small nodules within secondary lobules, probably each corresponding to an acinus.
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Tunaci, A., Berkmen, Y.M. & Gökmen, E. Pulmonary Gaucher's disease: High-resolution computed tomographic features. Pediatr Radiol 25, 237–238 (1995). https://doi.org/10.1007/BF02021548
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DOI: https://doi.org/10.1007/BF02021548