Abstract
We report the case of a 56-year-old man with severe normocomplementaemic primary urticarial vasculitis for 16 years. Nine and 11 years after the onset of the symptoms, he developed two severe neurological complications, seizure and transverse myelitis, that must be attributed to the vasculitis. Transverse myelitis has been reported in other systemic diseases, particularly lupus erythematosus, but this is the first case of transverse myelitis complicating urticarial vasculitis.
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References
Fauci AS, Haynes BF, Katz P. The spectrum of vasculitis. Ann Intern Med 1978;89:660–76.
Lie JT. Classification of vasculitis, 1815 to 1991. J Rheumatol 1992;19:83–9.
Lie JT. Nomenclature and classification of vasculitis: plus ça change, plus c'est la même chose. Arthritis Rheum 1994;37:181–6.
Asherson RA, Cruz DD, Stephens CJ, Mc Kee PH, Hughes GR. Urticarial vasculitis in a connective tissue disease: patterns, presentations and treatment. Semin Arthritis Rheum 1991; 20:285–96.
Mehregan DR, Hall MJ, Gibson LE. Urticarial vasculitis: a histopathologic and clinical review of 72 cases. J Am Acad Dermatol 1992;26:441–8.
Pasero G, Olivieri I, Gemignani G, Vitali C. Urticarial/arthritis syndrome: report of four B51 positive patients. Ann Rheum Dis 1989;48:508–11.
Alarcon-Segovia D. Primary antiphospholipid syndrome. J Rheumatol 1992, 19, 1778–81.
Chevalier X, Belmatoug N, Kahn MF. Seronegative leucocytoclastic vasculitis preceding the onset of disseminated systemic lupus. Rev Rhum Mal Osteo 1990;57:779–83.
Lipton HL, Yeasdall RD. Acute transverse myelopathy in adults. Arch Neurol 1978;4:51–9.
Lavalle C, Pizarro S, Drenkard C, Sanchez-Guerrero J, Alarcon-Segovia D. Transverse myelitis: a manifestation of systemic lupus erythematosous strongly associated with antiphospholipid anti-bodies. J Rheumatol 1990;17:34–7.
Staub HL, Capobianco K, Neto P R, Keiserman M. Rheumatoid arthritis, transverse myelitis and antiphospholipid antibodies. Clin Exp Rheumatol 1992;10:626–7.
Asherson RA, Sontheimer R. Urticarial vasculitis and syndromes in association with connective tissue diseases. Ann Rheum Dis 1991;50:743–4.
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Bolla, G., Disdier, P., Verrot, D. et al. Acute transverse myelitis and primary urticarial vasculitis. Clin Rheumatol 17, 250–252 (1998). https://doi.org/10.1007/BF01451059
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DOI: https://doi.org/10.1007/BF01451059