Summary
Two cases of biopsy-proven Alexander's disease are described with computed tomographic changes which, in our experience and on survey of the literature, have not occurred in any other condition. Such changes in a child with a progressive condition consistent with Alexander's disease, strongly support the diagnosis.
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Holland, I.M., Kendall, B.E. Computed tomography in Alexander's disease. Neuroradiology 20, 103–106 (1980). https://doi.org/10.1007/BF00339556
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DOI: https://doi.org/10.1007/BF00339556