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Retinal angiomatosis — von Hippel-Lindau’s Disease

  • Chapter
Vascular Tumors and Malformations of the Ocular Fundus

Part of the book series: Monographs in Ophthalmology ((MIOP,volume 14))

Abstract

The first reports on retinal angiomatosis are attributed to Magnus (1874), Jackson (1878), and Panas and Remy (1879) [58, 43, 65]. Fuchs (1882) published the description and drawings of the classical red peripheral tumor with the typically dilated artery and veins, but considered the lesion to be an arterio-venous aneurysm [23]. Collins (1894) gave the first pathological description of thin-walled vessels and cystic spaces, but called it a capillary naevus [15], while Czermak (1905) described it as a capillary angioma [16]. von Hippel (1911) identified the tumor as a hemangioblastoma and gave it the name of angiomatosis retinae [86]. In later years the entity was described by some authors as angiogliosis or angiogliomatosis [10, 27, 39]. In his classical paper Lindau (1926–1927) described the lesion as a primary hemangioma, noted the association of angiomatosis retinae with cerebellar cysts and proved the histological similarity of both cerebellar and retinal tumors [54, 55]. Van Der Hoeve (1932) finally classified the lesion among the congenital phakomatoses [85]. The disease has since been the subject of many publications under the denomination of angiomatosis retinae or von Hippel-Lindau’s disease.

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  1. Department of Ophthalmology, University Hospital, Ghent, Belgium

    J. J. De Laey & M. Hanssens

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© 1990 Belgian Society of Ophthalmology, Leuven, Belgium and Kluwer Academic Publishers

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De Laey, J.J., Hanssens, M. (1990). Retinal angiomatosis — von Hippel-Lindau’s Disease. In: Vascular Tumors and Malformations of the Ocular Fundus. Monographs in Ophthalmology, vol 14. Springer, Dordrecht. https://doi.org/10.1007/978-94-009-0589-4_2

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