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Spontaeous capsular ruptures in alport syndrome

  • Original Article
  • Published:
Annals of Ophthalmology

Abstract

Alport syndrome is an inherited disorder affecting the basement membranes, predominantly of the kidneys, eyes, and ears. In our series of 8 patients, anterior lenticonus was the most common ocular feature, as is typical in these cases. However, spontaneous capsular rupture was the presenting feature in 3 patients, rarely reported in Alport syndrome. On follow-up (3 months), all had spontaneous rupture of the lenticonus in the other eye.

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Authors and Affiliations

  1. Kasturba Medical College, OEU Institute of Ophthalmology, 576119, Manipal, India

    K. R. Sathish DOMS, MS.N,  Chandrashekar DOMS, MS, Vijaya Pai DOMS, MS, Prashant Bhatia MS & Gaurav Kakkar DOMS, MS

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  1. K. R. Sathish DOMS, MS.N
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  2. Chandrashekar DOMS, MS
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  3. Vijaya Pai DOMS, MS
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  4. Prashant Bhatia MS
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  5. Gaurav Kakkar DOMS, MS
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Sathish, K.R., Chandrashekar, Pai, V. et al. Spontaeous capsular ruptures in alport syndrome. Ann Ophthalmol 33, 131–135 (2001). https://doi.org/10.1007/s12009-001-0008-y

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