Abstract
Henoch–Scho¨nlein purpura (HSP) is the most common vasculitis in children. It is a multisystemic disease but pulmonary haemorrhage is extremely rare. We present the case of a 6-year-old boy with Henoch–Scho¨nlein purpura, pulmonary haemorrhage and severe renal involvement. The patient responded to a combination of intravenous methylprednisolone and cyclophosphamide. A review of the literature revealed that young age may be a good prognostic sign and that immunosuppressive drugs and supportive management are essential in the treatment. Renal biopsy is helpful in the differential diagnosis of HSP-mimicking pulmonary vasculitic syndromes. Combining cyclophosphamide with glucocorticoids may improve the outcome in severe HSP cases with pulmonary haemorrhage.
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Received: 5 July 2000 / Accepted: 2 February 2001
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Besbas, N., Duzova, A., Topaloglu, R. et al. Pulmonary Haemorrhage in a 6-Year-Old Boy with Henoch–Scho¨nlein Purpura. Clin Rheumatol 20, 293–296 (2001). https://doi.org/10.1007/PL00011205
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DOI: https://doi.org/10.1007/PL00011205