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Makrodaktylie

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Orthopädie und Unfallchirurgie

Part of the book series: Springer Reference Medizin ((SRM))

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Zusammenfassung

Der Begriff Makrodaktylie umfasst eine Vielzahl inhomogener Krankheitsbilder, die zu einer isolierten, disproportionalen Vergrößerung eines oder mehrerer Finger führen. Es handelt sich um eine sehr seltene, spontan auftretende, meistens einseitige Erkrankung. Die betroffenen Finger zeigen eine nervenbedingte Weichteilverdickung, die zu Achsabweichungen und Bewegungseinschränkungen sowie kosmetischen Problemen führen können. Die Erkrankung muss differenzialdiagnostisch von anderen Formen der Extremitätenvergrößerung wie z. B. fibröser Dysplasie, Klippel-Trénaunay-Syndrom, Maffucci-Syndrom oder Proteus-Syndrom unterschieden werden. In Fällen mit Funktionseinschränkung und/oder inakzeptabler kosmetischer Situation ist eine operative Intervention sinnvoll, auch wenn eine völlige Normalisierung der Kosmetik nicht zu erwarten ist. Gängige operative Maßnahmen umfassen die Strahlresektion, Weichteilreduktionsplastiken, Epiphysiodesen und Verkürzungsosteotomien.

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Authors and Affiliations

  1. Abteilung für Kinderorthopädie und Fußchirurgie, Orthopädisches Spital Speising, Wien, Österreich

    Sebastian Farr

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  1. Sebastian Farr
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Correspondence to Sebastian Farr .

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Editors and Affiliations

  1. Klinik für Orthopädie, Klinikum Osnabrück GmbH Klinik für Orthopädie, Osnabrück, Niedersachsen, Deutschland

    Martin Engelhardt

  2. Unfallchirurgie, Universitätsklinikum Münster Unfallchirurgie, Münster, Nordrhein-Westfalen, Deutschland

    Michael Raschke

Section Editor information

  1. Klinik für Orthopädie, Klinikum Stuttgart – Olgahospital, Stuttgart, Deutschland

    Thomas Wirth

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© 2022 Springer-Verlag GmbH Deutschland, ein Teil von Springer Nature

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Farr, S. (2022). Makrodaktylie. In: Engelhardt, M., Raschke, M. (eds) Orthopädie und Unfallchirurgie. Springer Reference Medizin. Springer, Berlin, Heidelberg. https://doi.org/10.1007/978-3-642-54673-0_115-1

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  • DOI: https://doi.org/10.1007/978-3-642-54673-0_115-1

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  • Print ISBN: 978-3-642-54673-0

  • Online ISBN: 978-3-642-54673-0

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