Abstract
For more in-depth research into congenital cardiac disease, such as for multicentric analysis of outcomes or stratification of risk for interventions, there is a need for a uniform and detailed system of nomenclature. The advances in digital technology and communication seen over the last quarter century have facilitated the task of standardization of entry of data and exchange of information.
In this chapter, the authors, as members of the International Society for Nomenclature of Paediatric and Congenital Heart Disease (ISNPCHD), review the principles and challenges of developing a standardized system of nomenclature for congenital heart disease, from the point of view of developing the International Paediatric and Congenital Cardiac Code (IPCCC) and the congenital heart list for the newest iteration of the International Classification of Diseases of the World Health Organization (ICD-11). The authors expand upon certain areas of contention, summarizing some of the discussions that have taken place among those seeking to create a standardized and international system for naming the various lesions encountered in patients presenting with congenital cardiac disease.
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Béland, M.J., Franklin, R.C., Aiello, V.D., Houyel, L., Weinberg, P.M., Anderson, R.H. (2020). Nomenclature and Classification of Cardiac Defects. In: da Cruz, E., Ivy, D., Hraska, V., Jaggers, J. (eds) Pediatric and Congenital Cardiology, Cardiac Surgery and Intensive Care. Springer, London. https://doi.org/10.1007/978-1-4471-4999-6_251-2
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DOI: https://doi.org/10.1007/978-1-4471-4999-6_251-2
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Latest
Nomenclature and Classification of Cardiac Defects- Published:
- 11 June 2020
DOI: https://doi.org/10.1007/978-1-4471-4999-6_251-2
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Original
Nomenclature and Classification of Cardiac Defects- Published:
- 08 August 2016
DOI: https://doi.org/10.1007/978-1-4471-4999-6_251-1